cholestasis-pigmentary retinopathy-cleft palate syndrome

MeSH: C535632ORPHA: 1415

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with cholestasis-pigmentary retinopathy-cleft palate syndrome, sourced from HPO and Orphanet clinical annotations.

Orofacial cleftPreauricular skin tagPreauricular pitAbnormal pinna morphologyPigmentary retinopathyCardiomyopathyCoarctation of aortaIntestinal malrotationAbnormality of the biliary systemShort statureAbnormal gallbladder morphologyCyst of the ductus choledochusVesicoureteral refluxHydronephrosisVaginal atresiaCongenital diaphragmatic herniaVentricular septal defectAtrial septal defectPatent ductus arteriosusConstipationAnal atresiaMeckel diverticulumAortic aneurysmEctopic ureteral orifice

Classification & Codes

MeSH Code

C535632

Orphanet Code

ORPHA:1415
cholestasis-pigmentary retinopathy-cleft palate syndrome
MeSHC535632
OrphanetORPHA:1415
Treatments0 drug(s)
Symptoms on record24 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO