chromosome 18q deletion syndrome

MeSH: C536580ORPHA: 1600

Overview

human disease

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with chromosome 18q deletion syndrome, sourced from HPO and Orphanet clinical annotations.

MicropenisMandibular prognathiaMacrotiaAbnormal retinal morphologyMyopiaAbnormal palmar dermatoglyphicsArachnodactylyTapered fingerIntellectual disabilityMild intellectual disabilityGlobal developmental delayNeonatal hypotoniaGrowth delayPatent ductus arteriosusTalipes equinovarusPes planusAbnormal facial shapeIncoordinationDownturned corners of mouthDelayed skeletal maturationKyphoscoliosisShort staturePulmonary valve defectsDepressed nasal bridgeDiffuse white matter abnormalitiesSecondary growth hormone deficiencyBilateral conductive hearing impairmentBilateral cryptorchidismAbnormal myelinationWide mouthOpen mouthHigh palateHydrocephalusMicrocephalyEpicanthusLow anterior hairlineShort philtrumSensorineural hearing impairmentBulbous noseProminent noseChoanal stenosisStrabismusDownslanted palpebral fissuresPectus excavatumHypothyroidismSeizureChoreoathetosisCerebellar hypoplasiaJoint hypermobilityFailure to thriveSlender buildCongestive heart failureAortic valve stenosisMitral regurgitationSecundum atrial septal defectDecreased circulating IgA concentrationBiparietal narrowingAortic aneurysmAbsence of the pulmonary valveDysplastic pulmonary valveLeft aortic arch with right descending aorta and right ductus arteriosusLeft-to-right shuntThick vermilion borderAtlantoaxial abnormalityAstrocytoma

Classification & Codes

MeSH Code

C536580

Orphanet Code

ORPHA:1600
chromosome 18q deletion syndrome
MeSHC536580
OrphanetORPHA:1600
Treatments0 drug(s)
Symptoms on record65 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO