chronic pneumonitis of infancy

ORPHA: 91359

Overview

Chronic pneumonitis of infancy is a rare pediatric form of interstitial lung disease (ILD, see this term)

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with chronic pneumonitis of infancy, sourced from HPO and Orphanet clinical annotations.

Failure to thriveDiffuse reticular or finely nodular infiltrationsHyperventilationHypoxemiaCoughGround-glass opacificationReduced forced vital capacityCyanosisFeverRespiratory distressTachypneaIntercostal retractionsMediastinal lymphadenopathy

Classification & Codes

Orphanet Code

ORPHA:91359
chronic pneumonitis of infancy
OrphanetORPHA:91359
Treatments0 drug(s)
Symptoms on record13 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO