Chronic Thromboembolic Pulmonary Hypertension

ORPHA: 70591

Overview

medical condition

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with Chronic Thromboembolic Pulmonary Hypertension, sourced from HPO and Orphanet clinical annotations.

Congestive heart failurePulmonary arterial hypertensionIncreased pulmonary vascular resistancePalpitationsPulmonary embolismDeep venous thrombosisReduced vital capacityExertional dyspneaFatigueReduced FEV1/FVC ratioDepressionEdemaSyncopeObesityCardiac shuntRight ventricular failureAbnormality of blood and blood-forming tissuesAutoimmunityAntiphospholipid antibody positivityRecurrent thromboembolismRight ventricular dilatationAbnormal T-waveAbnormal left ventricular functionCentral sleep apneaElevated circulating C-reactive protein concentrationComplete right bundle branch blockDysfibrinogenemiaAbnormality of von Willebrand factorIncreased HDL cholesterol concentrationHypocapniaLupus anticoagulantRight atrial enlargementIncreased factor VIII activityInflammation of the large intestineNeoplasmOsteomyelitisMyeloproliferative disorder

Classification & Codes

Orphanet Code

ORPHA:70591
Chronic Thromboembolic Pulmonary Hypertension
OrphanetORPHA:70591
Treatments0 drug(s)
Symptoms on record37 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO