Churg-Strauss syndrome

MeSH: D015267ORPHA: 183

Overview

a systemic vasculitis realized as blood vessel inflammation, with symptoms asthma along with hay fever, rash and gastrointestinal bleeding

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with Churg-Strauss syndrome, sourced from HPO and Orphanet clinical annotations.

SinusitisPurpuraUrticariaWeight lossIncreased total eosinophil countAsthmaPulmonary infiltratesVasculitisAutoimmunityCentral nervous system degenerationPeripheral neuropathyIncreased inflammatory responseHematuriaHypertensionSkin rashHypopigmented skin patchesGait disturbanceHypertrophic cardiomyopathyAbnormal pericardium morphologyTubulointerstitial nephritisDysphagiaNausea and vomitingAbdominal painAbnormal pleura morphologyArthralgiaRheumatoid factor positiveIncreased circulating IgE concentrationVenous thrombosisAirway obstructionFatigueMultiple mononeuropathyEosinophilic pneumoniaCytoplasmic antineutrophil antibody positivityAnti-proteinase 3 antibody positivityAnti-myeloperoxidase antibody positivityAnti-neutrophil elastase antibody positivityRenal insufficiencyProteinuriaCutis marmorataAcrocyanosisArthritisSubcutaneous noduleCongestive heart failureMyocardial infarctionFeverGastroesophageal refluxMalabsorptionRespiratory insufficiencyHemoptysisPleural effusionTransient ischemic attackMyalgiaHemiplegia/hemiparesisIntestinal obstructionRecurrent intrapulmonary hemorrhageCranial nerve paralysisCrescentic glomerulonephritisCoughMyocarditisGastrointestinal eosinophiliaNasal polyposisEndocarditisMyositisGlomerulopathyPapuleCutaneous granuloma

Classification & Codes

MeSH Code

D015267

Orphanet Code

ORPHA:183
Churg-Strauss syndrome
MeSHD015267
OrphanetORPHA:183
Treatments0 drug(s)
Symptoms on record66 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO