Cogan syndrome
MeSH: D055952ORPHA: 1467
Overview
a rare vasculitis of children and young adults characterized by nonsyphilitic interstitial keratitis of cornea, fever and fatigue.
Available Treatments (0)
No treatments linked yet
Clinical trials or compassionate use may be available — consult a specialist.
Clinical Presentation
Signs and symptoms associated with Cogan syndrome, sourced from HPO and Orphanet clinical annotations.
TinnitusKeratitisPhotophobiaAbnormal vestibular functionVertigoReduced visual acuitySensorineural hearing impairmentThrombocytosisAnemiaIncreased total leukocyte countElevated erythrocyte sedimentation rateInflammatory abnormality of the eyeConjunctivitisUveitisBlindnessAortic regurgitationVasculitisLarge vessel vasculitisScleritisEpiscleritis
Classification & Codes
MeSH Code
D055952Orphanet Code
ORPHA:1467Cogan syndrome
| MeSH | D055952 |
| Orphanet | ORPHA:1467 |
| Treatments | 0 drug(s) |
| Symptoms on record | 20 signs |
| Status | published |
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO