Cold agglutinin disease
ICD-10: D59.1ORPHA: 90033
Overview
type of autoimmune hemolytic anemia
Available Treatments (0)
No treatments linked yet
Clinical trials or compassionate use may be available — consult a specialist.
Clinical Presentation
Signs and symptoms associated with Cold agglutinin disease, sourced from HPO and Orphanet clinical annotations.
PallorAutoimmune hemolytic anemiaHeadacheExertional dyspneaAutoimmunityFatigueSplenomegalyReticulocytosisPalpitationsArthralgiaHemoglobinuriaMicrospherocytosisLymphoproliferative disorderUnconjugated hyperbilirubinemiaDecreased hemoglobin concentrationReduced haptoglobin levelIncreased circulating lactate dehydrogenase concentrationPositive direct antiglobulin testJaundiceCongestive heart failureTachycardiaFeverSystemic lupus erythematosusChronic lymphatic leukemiaAbnormal urinary colorElevated jugular venous pressureChest pain
Classification & Codes
ICD-10 Code
D59.1Orphanet Code
ORPHA:90033Cold agglutinin disease
| ICD-10 | D59.1 |
| Orphanet | ORPHA:90033 |
| Treatments | 0 drug(s) |
| Symptoms on record | 27 signs |
| Status | published |
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO