congenital absence of upper arm and forearm with hand present

ORPHA: 294975

Overview

congenital malformation in which the upper portion of a limb is either shortened or absent

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with congenital absence of upper arm and forearm with hand present, sourced from HPO and Orphanet clinical annotations.

Abnormal heart morphologyUpper limb phocomeliaAbnormality of the musculoskeletal systemAbnormal thorax morphologyAbnormality of the vertebral columnAbnormal cardiac septum morphologyAbnormality of the faceAbnormality of the neckCongenital malformation of the great arteriesAbnormal lung morphologyCleft palateRenal agenesisAbnormal hip bone morphologyPolydactylySyndactylySmall for gestational ageAtypical scarring of skin

Classification & Codes

Orphanet Code

ORPHA:294975
congenital absence of upper arm and forearm with hand present
OrphanetORPHA:294975
Treatments0 drug(s)
Symptoms on record17 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO
congenital absence of upper arm and forearm with hand present | OrphanDrug