congenital aortic stenosis
ICD-10: Q23.0ORPHA: 3093
Overview
human disease
Available Treatments (0)
No treatments linked yet
Clinical trials or compassionate use may be available — consult a specialist.
Clinical Presentation
Signs and symptoms associated with congenital aortic stenosis, sourced from HPO and Orphanet clinical annotations.
Aortic valve stenosisExertional dyspneaHeart murmurLeft ventricular hypertrophyAortic valve calcificationAbnormal T-waveDysplastic aortic valveAortic valve atresiaIncreased QRS voltageAngina pectorisEndocardial fibroelastosisAbnormal left ventricular functionReduced left ventricular ejection fractionAbnormal pulse pressureEndocarditisSudden cardiac deathThoracic aortic aneurysm
Classification & Codes
ICD-10 Code
Q23.0Orphanet Code
ORPHA:3093congenital aortic stenosis
| ICD-10 | Q23.0 |
| Orphanet | ORPHA:3093 |
| Treatments | 0 drug(s) |
| Symptoms on record | 17 signs |
| Status | published |
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO