congenital aortic stenosis

ICD-10: Q23.0ORPHA: 3093

Overview

human disease

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with congenital aortic stenosis, sourced from HPO and Orphanet clinical annotations.

Aortic valve stenosisExertional dyspneaHeart murmurLeft ventricular hypertrophyAortic valve calcificationAbnormal T-waveDysplastic aortic valveAortic valve atresiaIncreased QRS voltageAngina pectorisEndocardial fibroelastosisAbnormal left ventricular functionReduced left ventricular ejection fractionAbnormal pulse pressureEndocarditisSudden cardiac deathThoracic aortic aneurysm

Classification & Codes

ICD-10 Code

Q23.0

Orphanet Code

ORPHA:3093
congenital aortic stenosis
ICD-10Q23.0
OrphanetORPHA:3093
Treatments0 drug(s)
Symptoms on record17 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO