congenital disorder of glycosylation Ip

ORPHA: 280071

Overview

human disease

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with congenital disorder of glycosylation Ip, sourced from HPO and Orphanet clinical annotations.

Intellectual disabilitySeizureGlobal developmental delayAbnormal isoelectric focusing of serum transferrinType I transferrin isoform profileFloppy infantReduced social responsivenessMicrocephalyHearing impairmentAbnormality of visionHypertoniaHyperreflexiaAbnormal facial shapeFeeding difficultiesRetrognathiaLong philtrumHigh foreheadStrabismusDry skinAtaxiaFailure to thriveCerebral atrophyOpisthotonusGray matter heterotopiaHypokinesiaAbnormal cerebral white matter morphologyLimb hypertoniaEpisodic vomitingScoliosisElevated circulating hepatic transaminase concentrationInverted nipplesTemperature instabilityDecreased corneal reflexAxial hypotoniaAbnormal adipose tissue morphologyEEG with burst suppressionAbnormal skeletal morphologyDelayed myelinationWidened subarachnoid spaceCerebral white matter atrophy

Classification & Codes

Orphanet Code

ORPHA:280071
congenital disorder of glycosylation Ip
OrphanetORPHA:280071
Treatments0 drug(s)
Symptoms on record40 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO