congenital heart block

ICD-10: Q24.6MeSH: C535758ORPHA: 60041

Overview

atrioventricular block characterized by the presence of conduction system disease of any form, which is diagnosed on or before 28 days of life

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with congenital heart block, sourced from HPO and Orphanet clinical annotations.

Atrioventricular blockThird degree atrioventricular blockPremature birthVaginal birth after CaesareanCyanosisHyperhidrosisPallorSyncopeIntrauterine growth retardationOligohydramniosWeak cryCongestive heart failurePatent ductus arteriosusPatent foramen ovaleBradycardiaPericardial effusionHydrops fetalisExercise intoleranceProlonged QTc intervalFeeding difficulties in infancySecond degree atrioventricular blockFatiguePeripheral edemaCracklesGallop rhythmEndocardial fibroelastosisPleural effusionFirst degree atrioventricular blockAbnormal heart valve physiology

Classification & Codes

ICD-10 Code

Q24.6

MeSH Code

C535758

Orphanet Code

ORPHA:60041
congenital heart block
ICD-10Q24.6
MeSHC535758
OrphanetORPHA:60041
Treatments0 drug(s)
Symptoms on record29 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO