congenital hydrocephalus

ORPHA: 2185

Overview

Hydrocephalus that is present at birth

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with congenital hydrocephalus, sourced from HPO and Orphanet clinical annotations.

HydrocephalusMacrocephalyFacial asymmetryPosteriorly rotated earsBulbous noseStrabismusDownslanted palpebral fissuresIris colobomaIntellectual disabilitySeizureMotor delayFrontal bossingVentriculomegalySmall cerebral cortexAbnormal cortical gyrationColpocephalySensorineural hearing impairmentOptic atrophyMacular hypoplasiaLissencephalyAbnormal heart morphology

Classification & Codes

Orphanet Code

ORPHA:2185
congenital hydrocephalus
OrphanetORPHA:2185
Treatments0 drug(s)
Symptoms on record21 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO