congenital hypothyroidism due to transplacental passage of maternal TSH-binding inhibitory antibodies

ORPHA: 95715

Overview

Congenital hypothyroidism due to transplacental passage of maternal thyroid-stimulating hormone (TSH)-binding inhibitory antibodies is a type of transient congenital hypothyroidism (see this term), a thyroid hormone deficiency that is not permanent

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with congenital hypothyroidism due to transplacental passage of maternal TSH-binding inhibitory antibodies, sourced from HPO and Orphanet clinical annotations.

Autoimmune antibody positivityWide anterior fontanelDry skinHyporeflexiaUmbilical herniaConstipationAbnormality of thyroid physiologyFeeding difficultiesDecreased thyroid-stimulating hormone levelReduced radioactive iodine uptakeDecreased circulating T4 concentrationExcessive daytime somnolenceCoarse facial featuresNeonatal hypotoniaConjugated hyperbilirubinemiaProlonged neonatal jaundiceAnti-thyroid peroxidase antibody positivityAbnormal circulating thyroglobulin concentrationMoon facies

Classification & Codes

Orphanet Code

ORPHA:95715
congenital hypothyroidism due to transplacental passage of maternal TSH-binding inhibitory antibodies
OrphanetORPHA:95715
Treatments0 drug(s)
Symptoms on record19 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO