congenital insensitivity to pain with anhidrosis

ORPHA: 642

Overview

rare disease

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with congenital insensitivity to pain with anhidrosis, sourced from HPO and Orphanet clinical annotations.

Self-mutilationAnhidrosisIntellectual disabilityRecurrent Staphylococcus aureus infectionsOsteomyelitisAbnormality of peripheral nerve conductionPain insensitivityImpaired temperature sensationAplasia of the sweat glandsDry skinAtypical scarring of skinSpecific learning disabilityRecurrent feverPainless fractures due to injuryNeuropathic arthropathyTrophic limb changesAbnormality of humoral immunityPremature loss of teethNail-bitingAbscessAbnormality of lower limb jointFasciitisLichenificationShort attention spanHyperactivityBruising susceptibilitySyncopeGrowth delayAnemiaUnexplained feversDysphagiaRecurrent aspiration pneumoniaAbnormality of the autonomic nervous systemDistal sensory impairmentAbnormality of the ankleSeptic arthritisAbnormal hip bone morphologySomatic sensory dysfunctionFunctional motor deficitOrthostatic hypotension due to autonomic dysfunctionDecreased corneal reflexAlveolar ridge overgrowthAvascular necrosisFeeding difficultiesTooth abscessTongue painImpulsivityAbnormal lumbar spine morphologyAbnormal emotional stateCorneal scarringHyperhidrosisHypothermiaChronic kidney diseaseCorneal ulcerationHyperesthesiaGait disturbance

Classification & Codes

Orphanet Code

ORPHA:642
congenital insensitivity to pain with anhidrosis
OrphanetORPHA:642
Treatments0 drug(s)
Symptoms on record56 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO
congenital insensitivity to pain with anhidrosis | OrphanDrug