congenital malabsorptive diarrhea 4

MeSH: C563673ORPHA: 83620

Overview

congenital diarrhea characterized by chronic unremitting malabsorptive diarrhea and a profound dysgenesis of the enteroendocrine cells that has material basis in mutation in the gene encoding neurogenin-3 (NEUROG3) on chromosome 10q21.3

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with congenital malabsorptive diarrhea 4, sourced from HPO and Orphanet clinical annotations.

DehydrationVomitingDiarrheaMalabsorptionHyperchloremic metabolic acidosisPortal hypertensionCholestatic liver diseaseAbnormal cellular phenotypeType I diabetes mellitus

Classification & Codes

MeSH Code

C563673

Orphanet Code

ORPHA:83620
congenital malabsorptive diarrhea 4
MeSHC563673
OrphanetORPHA:83620
Treatments0 drug(s)
Symptoms on record9 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO