Congenital self-healing reticulohistiocytosis

MeSH: C535843ORPHA: 99872

Overview

Hashimoto-Pritzker histiocytosis (HPH) is a variant of Langerhans cell histiocytosis (see this term) characterized by multiple disseminated skin lesions (firm, red-brown, painless papulo-nodules)

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Classification & Codes

MeSH Code

C535843

Orphanet Code

ORPHA:99872
Congenital self-healing reticulohistiocytosis
MeSHC535843
OrphanetORPHA:99872
Treatments0 drug(s)
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO