cortical blindness-intellectual disability-polydactyly syndrome

MeSH: C565674ORPHA: 1389

Overview

This syndrome is characterised by cortical blindness, intellectual deficit, and polydactyly

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with cortical blindness-intellectual disability-polydactyly syndrome, sourced from HPO and Orphanet clinical annotations.

Abnormal palate morphologyMicroretrognathiaLong philtrumAbnormality of visual evoked potentialsPostaxial hand polydactylyIntellectual disabilityHypertoniaHyperreflexiaRecurrent respiratory infectionsShort noseShort statureCachexiaProminent foreheadCerebral visual impairment

Classification & Codes

MeSH Code

C565674

Orphanet Code

ORPHA:1389
cortical blindness-intellectual disability-polydactyly syndrome
MeSHC565674
OrphanetORPHA:1389
Treatments0 drug(s)
Symptoms on record14 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO