cutaneous small-vessel vasculitis
ORPHA: 8892 Treatments Available
Overview
hypersensitivity vasculitis that results in inflammation of small blood vessels, characterized clinically by palpable purpura, which is a slightly elevated purpuric rash over one or more areas of the skin
Available Treatments (2)
| Drug | Form | Status | Countries | Lead Time |
|---|---|---|---|---|
| rituximab Orphan Cold Chain | IV infusion 10mg/mL (100mg/10mL, 500mg/50mL vials) | FDA Approved | 11 | 14d |
| prednisone | oral tablet 1mg, 2.5mg, 5mg, 10mg, 20mg, 50mg; oral solution 5mg/5mL | FDA Approved | 13 | 1d |
Clinical Presentation
Signs and symptoms associated with cutaneous small-vessel vasculitis, sourced from HPO and Orphanet clinical annotations.
Abnormal oral cavity morphologyCutis marmorataPurpuraSkin rashUrticariaSubcutaneous noduleRecurrent skin infectionsFeverVasculitisArthralgiaMyalgiaErythemaGangrenePapule
Classification & Codes
Orphanet Code
ORPHA:889cutaneous small-vessel vasculitis
| Orphanet | ORPHA:889 |
| Treatments | 2 drug(s) |
| Symptoms on record | 14 signs |
| Status | published |
Treatment Summary
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO