Danon disease

ICD-10: E74.0MeSH: D052120ORPHA: 34587

Overview

Human disease

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with Danon disease, sourced from HPO and Orphanet clinical annotations.

Intellectual disabilityGait disturbanceHypertrophic cardiomyopathyDilated cardiomyopathyCardiorespiratory arrestMuscle flaccidity

Classification & Codes

ICD-10 Code

E74.0

MeSH Code

D052120

Orphanet Code

ORPHA:34587
Danon disease
ICD-10E74.0
MeSHD052120
OrphanetORPHA:34587
Treatments0 drug(s)
Symptoms on record6 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO