delayed speech-facial asymmetry-strabismus-ear lobe creases syndrome

ORPHA: 3038

Overview

This syndrome is extremely rare and is characterized by delayed speech development, mild facial asymmetry, strabismus and transverse ear lobe creases

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with delayed speech-facial asymmetry-strabismus-ear lobe creases syndrome, sourced from HPO and Orphanet clinical annotations.

High palateHypertelorismFacial asymmetryLong philtrumLow-set earsAnteverted naresStrabismusDownslanted palpebral fissuresPtosisExotropiaDelayed speech and language developmentIntellectual disabilityUnilateral narrow palpebral fissureAnterior creases of earlobe

Classification & Codes

Orphanet Code

ORPHA:3038
delayed speech-facial asymmetry-strabismus-ear lobe creases syndrome
OrphanetORPHA:3038
Treatments0 drug(s)
Symptoms on record14 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO