Denys-Drash syndrome

MeSH: D030321ORPHA: 220

Overview

Human disease

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with Denys-Drash syndrome, sourced from HPO and Orphanet clinical annotations.

Male pseudohermaphroditismProteinuriaNephrotic syndromeNephropathyNephroblastomaHypertensionGonadal dysgenesis

Classification & Codes

MeSH Code

D030321

Orphanet Code

ORPHA:220
Denys-Drash syndrome
MeSHD030321
OrphanetORPHA:220
Treatments0 drug(s)
Symptoms on record7 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO
Denys-Drash syndrome | OrphanDrug