dermatomyositis
ICD-10: M33.033.0-M33.133.1MeSH: D003882ORPHA: 221
Overview
myositis that results in inflammation located in muscle or located in skin where a skin rash is often seen prior to the onset of muscle weakness
Available Treatments (0)
No treatments linked yet
Clinical trials or compassionate use may be available — consult a specialist.
Clinical Presentation
Signs and symptoms associated with dermatomyositis, sourced from HPO and Orphanet clinical annotations.
Weight lossRespiratory insufficiencyRecurrent respiratory infectionsPulmonary fibrosisDiffuse reticular or finely nodular infiltrationsRespiratory insufficiency due to muscle weaknessArthralgiaElevated circulating hepatic transaminase concentrationElevated circulating creatine kinase concentrationEMG: myopathic abnormalitiesAbnormal pulmonary interstitial morphologyAbnormal hair quantityFatigueElevated circulating aldolase concentrationIncreased circulating lactate dehydrogenase concentrationGottron's papulesShawl signAnti-SUMO-activating enzyme subunit 1 antibody positivityAnti-SUMO-activating enzyme subunit 2 antibody positivityHeliotrope rashMyositisPapuleSkin ulcerCutaneous photosensitivityPoikilodermaAlopeciaDysphoniaMyocardial infarctionAbnormal eyelid morphologyEdemaAutoimmunityLimb-girdle muscle weaknessMyalgiaEMG abnormalityProximal muscle weaknessInflammatory myopathyErythemaPeriorbital edemaChondrocalcinosisDry skinSkin rashPruritusFacial erythemaAcrocyanosisHypotoniaArthritisAbnormal nail morphologyPericarditisAbnormal eosinophil morphologyFeverDysphagiaPulmonary arterial hypertensionVasculitisNeoplasmLymphomaBreast carcinomaAplasia/Hypoplasia of the skinFeeding difficulties in infancyArrhythmiaSinus tachycardiaMyocarditisV-signLung adenocarcinomaRaynaud phenomenonAnti-MDA5 antibody positivityAnti-Mi2 antibody positivityAnti-transcription intermediary factor-1gamma antibody positivityAnti-SUMO-activating enzyme antibody positivityAnti-nuclear matrix protein-2 antibody positivityAnti-histidyl tRNA synthetase antibody positivityTelangiectasia of the skinCellulitisGastrointestinal stroma tumorGangreneGottron signHolster signPalmar hyperkeratosisMuscle weaknessGottron's sign
Classification & Codes
ICD-10 Code
M33.033.0-M33.133.1MeSH Code
D003882Orphanet Code
ORPHA:221dermatomyositis
| ICD-10 | M33.033.0-M33.133.1 |
| MeSH | D003882 |
| Orphanet | ORPHA:221 |
| Treatments | 0 drug(s) |
| Symptoms on record | 79 signs |
| Status | published |
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO