diastematomyelia
ICD-10: Q06.2ORPHA: 1671
Overview
rare congenital abnormality in which the spinal cord is split in half by fibrous or bony tissue. It may present as an isolated phenomenon or in association with spina bifida
Available Treatments (0)
No treatments linked yet
Clinical trials or compassionate use may be available — consult a specialist.
Clinical Presentation
Signs and symptoms associated with diastematomyelia, sourced from HPO and Orphanet clinical annotations.
Generalized hirsutismScoliosisDiastomatomyelia
Classification & Codes
ICD-10 Code
Q06.2Orphanet Code
ORPHA:1671diastematomyelia
| ICD-10 | Q06.2 |
| Orphanet | ORPHA:1671 |
| Treatments | 0 drug(s) |
| Symptoms on record | 3 signs |
| Status | published |
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO