diffuse myelinoclastic sclerosis

ICD-10: G37.0MeSH: D002549ORPHA: 59298

Overview

a progressive demyelinating disorder of the central nervous system

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with diffuse myelinoclastic sclerosis, sourced from HPO and Orphanet clinical annotations.

HyperreflexiaHeadacheProgressive neurologic deteriorationIncreased CSF protein concentrationCNS demyelinationHyperintensity of cerebral white matter on MRIEsotropiaDiplopiaSeizureAtaxiaEncephalopathyMuscle weaknessVomitingNauseaPostural instabilityVertigoIncreased intracranial pressureAnkle clonusCSF pleocytosis

Classification & Codes

ICD-10 Code

G37.0

MeSH Code

D002549

Orphanet Code

ORPHA:59298
diffuse myelinoclastic sclerosis
ICD-10G37.0
MeSHD002549
OrphanetORPHA:59298
Treatments0 drug(s)
Symptoms on record19 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO