distal 10q deletion syndrome

MeSH: C567182ORPHA: 96148

Overview

Human disease

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with distal 10q deletion syndrome, sourced from HPO and Orphanet clinical annotations.

Cleft palateHigh palateMicrocephalyEpicanthusSmooth philtrumFacial asymmetryMicrognathiaLow-set earsProminent nasal bridgeProminent noseAstigmatismMyopiaUpslanted palpebral fissureOculomotor apraxiaAggressive behaviorSingle transverse palmar creaseBrachydactylyTapered fingerSeizureSpasticityCerebellar hypoplasiaFacial diplegiaPremature birthAtrial septal defectPatent ductus arteriosusPes planusSandal gapClonusDelayed speech and language developmentIntellectual disabilityGlobal developmental delaySpecific learning disabilityAbnormal facial shapeThin upper lip vermilionAbnormality of the outer earWide nasal bridgeStrabismusAtypical behaviorEnuresisFailure to thriveEnlarged cisterna magnaLower limb hyperreflexiaPoor speechRecurrent infectionsPostnatal growth retardationFloppy infantClinodactylyVesicoureteral refluxHorseshoe kidneyAbnormality of the genitourinary systemUnsteady gaitSleep disturbanceCavum septum pellucidumClinodactyly of the 5th fingerShort stature2-3 toe cutaneous syndactylyLateral ventricle dilatationPoor fine motor coordinationAttention deficit hyperactivity disorderInferior cerebellar vermis hypoplasiaPes valgusCongenital sensorineural hearing impairmentShort metatarsalFeeding difficultiesFunctional abnormality of the bladderBrachycephalyTriangular faceBroad foreheadNarrow foreheadWidow's peakProtruding earDownslanted palpebral fissuresProptosisHypotelorismAnxietyPectus excavatumProminent fingertip padsAtaxiaCraniosynostosisHip dysplasiaHypoplastic toenailsAcute kidney injuryFrontal bossingAnal atresiaHip dislocationLumbar hyperlordosisShort noseSpina bifida occultaScapular wingingProminent metopic ridgeCochlear malformationAbnormal morphology of the vestibule of the inner ear

Classification & Codes

MeSH Code

C567182

Orphanet Code

ORPHA:96148
distal 10q deletion syndrome
MeSHC567182
OrphanetORPHA:96148
Treatments0 drug(s)
Symptoms on record92 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO