distal monosomy 9p

ORPHA: 1642

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with distal monosomy 9p, sourced from HPO and Orphanet clinical annotations.

Posteriorly rotated earsShort noseMicrotiaAbnormal antihelix morphologyMidface retrusionHypospadiasHypoplastic labia majoraAbnormality of the dentitionEpicanthusBrachydactylyWide intermamillary distanceAplasia/Hypoplasia of the earlobesAbnormal helix morphologyEnlarged thoraxHerniaCleft palateAbnormal cardiovascular system morphologyTrigonocephalyHypertelorismWide nasal bridgeShort neckProptosisUpslanted palpebral fissureIntellectual disabilityHypotoniaGlobal developmental delayHigh, narrow palate

Classification & Codes

Orphanet Code

ORPHA:1642
distal monosomy 9p
OrphanetORPHA:1642
Treatments0 drug(s)
Symptoms on record27 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO