distal trisomy 18q

ORPHA: 1716

Overview

human disease

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with distal trisomy 18q, sourced from HPO and Orphanet clinical annotations.

CryptorchidismDolichocephalyRound faceTriangular faceMicrognathiaProminent nasal bridgeAnteverted naresShort neckThickened nuchal skin foldCarious teethGlobal developmental delayShort noseProgressive intervertebral space narrowingAbnormal dental morphologyAbnormal hair patternCognitive impairmentHigh palateArachnodactylyAbnormal dermatoglyphicsBilateral single transverse palmar creasesHypoplasia of penisAbnormal cardiovascular system morphologyCamptodactyly of fingerAbnormal female external genitalia morphologyChoanal atresiaIris colobomaPectus excavatumLarge handsDeviation of fingerClinodactyly of the 5th fingerPosteriorly rotated ears

Classification & Codes

Orphanet Code

ORPHA:1716
distal trisomy 18q
OrphanetORPHA:1716
Treatments0 drug(s)
Symptoms on record31 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO
distal trisomy 18q | OrphanDrug