dominant pericentral pigmentary retinopathy

MeSH: C566713ORPHA: 791

Overview

retinitis pigmentosa that is characterized pigmentary retinal degeneration with onset in the teens leading to blindness in the sixth ans seventh decades of life

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with dominant pericentral pigmentary retinopathy, sourced from HPO and Orphanet clinical annotations.

Conductive hearing impairmentSensorineural hearing impairmentVisual impairmentAbnormal electroretinogramRetinal degenerationPhotophobiaBlindnessNystagmusOptic atrophyProgressive night blindnessAbnormal retinal pigmentationSpicular pigmentation of the retinaAbnormal retinal vascular morphologyGlaucomaOptic disc pallorKeratoconusOphthalmoplegiaNyctalopiaHyperinsulinemiaRetinal atrophyPosterior subcapsular cataractAttenuation of retinal blood vesselsPeripheral visual field lossCystoid macular edemaOptic disc drusenAbnormal full-field electroretinogramAbnormal central response of multifocal electroretinogramPhotoreceptor outer segment loss on macular OCTColor vision defectReduced visual acuityPhotopsia

Classification & Codes

MeSH Code

C566713

Orphanet Code

ORPHA:791
dominant pericentral pigmentary retinopathy
MeSHC566713
OrphanetORPHA:791
Treatments0 drug(s)
Symptoms on record31 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO