Donohue syndrome

MeSH: D056731ORPHA: 508

Overview

Human disease

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with Donohue syndrome, sourced from HPO and Orphanet clinical annotations.

Insulin resistanceHyperkeratosisHypertrichosisFasting hypoglycemiaReduced subcutaneous adipose tissueSevere intrauterine growth retardationPostnatal growth retardationPostprandial hyperglycemiaLong penisLabial hypertrophyEnlarged kidneyHyperinsulinemiaAcanthosis nigricansIntellectual disabilityFailure to thriveHypertrophic cardiomyopathyFacial hypertrichosisHepatomegalySkeletal muscle atrophyOvergrowth of external genitaliaAbdominal distentionDecreased body weightProminent nipplesRecurrent infantile hypoglycemiaClitoral hypertrophySevere global developmental delayNephrocalcinosisMicrocephalyPointed chinHypertelorismLow-set earsProtruding earWide noseIncreased circulating renin concentrationIncreased circulating aldosterone concentrationHyperextensible skinThickened skinLarge handsLong footRectal prolapseHypercalciuriaHypokalemiaAxial hypotoniaCentral hypothyroidismThick vermilion borderMegarectumEnlarged ovaries

Classification & Codes

MeSH Code

D056731

Orphanet Code

ORPHA:508
Donohue syndrome
MeSHD056731
OrphanetORPHA:508
Treatments0 drug(s)
Symptoms on record47 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO
Donohue syndrome | OrphanDrug