dopamine beta-hydroxylase deficiency

MeSH: C535600ORPHA: 230

Overview

genetic metabolic disorder

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with dopamine beta-hydroxylase deficiency, sourced from HPO and Orphanet clinical annotations.

Orthostatic hypotensionBilateral ptosisElevated urinary dopamine levelRhinitisSyncopeReduced tendon reflexesAnemiaHypoglycemiaSleep disturbanceIncreased blood urea nitrogenElevated circulating creatinine concentrationExercise-induced muscle fatigueFatigueRetrograde ejaculationNocturiaBlurred visionHypotoniaDehydrationVomitingDiarrheaHypothermiaDyspneaVertigoAbnormal EKGOrthostatic syncopeChest painHyperinsulinemiaInsulin resistance

Classification & Codes

MeSH Code

C535600

Orphanet Code

ORPHA:230
dopamine beta-hydroxylase deficiency
MeSHC535600
OrphanetORPHA:230
Treatments0 drug(s)
Symptoms on record28 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO