double outlet left ventricle

ORPHA: 3427

Contents

1. Overview
2. Available Treatments
3. Clinical Presentation
4. Classification & Codes

Overview

Double-outlet left ventricle (DOLV) is an extremely rare congenital cardiac malformation in which both the aorta and the pulmonary artery arise, either exclusively or predominantly, from the morphologic left ventricle

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with double outlet left ventricle, sourced from HPO and Orphanet clinical annotations.

Double outlet left ventricleVentricular septal defectPatent ductus arteriosusAbnormal right ventricular functionCyanosisCardiomegalyTricuspid atresiaAbnormal coronary artery courseCryptorchidismOrofacial cleftHypertelorismFailure to thriveTachypneaSystolic heart murmurPulmonary artery stenosisBicuspid pulmonary valvePulmonary valve atresia

Classification & Codes

Orphanet Code

ORPHA:3427

double outlet left ventricle

Orphanet	`ORPHA:3427`
Treatments	0 drug(s)
Symptoms on record	17 signs
Status	published

Factual Authority

Last Updated3/20/2026

Clinical DataHPO · Orphanet

Drug DataFDA · EMA · CDSCO