dyschromatosis universalis hereditaria

MeSH: C535730ORPHA: 241

Overview

pigmentation disease characterized by reticulate hyper- and hypo-pigmentated macules in a generalized distribution

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with dyschromatosis universalis hereditaria, sourced from HPO and Orphanet clinical annotations.

Hearing impairmentCutaneous photosensitivityHypermelanotic maculeHypopigmented skin patchesFrecklingShort statureSpotty hypopigmentationMultiple cafe-au-lait spotsMacule

Classification & Codes

MeSH Code

C535730

Orphanet Code

ORPHA:241
dyschromatosis universalis hereditaria
MeSHC535730
OrphanetORPHA:241
Treatments0 drug(s)
Symptoms on record9 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO