dystonia 16

MeSH: C567430ORPHA: 210571

Overview

Dystonia 16 (DYT16) is a very rare and newly discovered movement disorder which is characterized by early-onset progressive limb dystonia, laryngeal and oromandibular dystonia, and parkinsonism

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with dystonia 16, sourced from HPO and Orphanet clinical annotations.

Limb dystoniaTorticollisDysarthriaParkinsonismHyperreflexiaDysphoniaDysphagiaBradykinesiaPostural tremorOrofacial dyskinesiaUnsteady gaitAbnormal pyramidal signLower limb painMotor delayIntellectual disability

Classification & Codes

MeSH Code

C567430

Orphanet Code

ORPHA:210571
dystonia 16
MeSHC567430
OrphanetORPHA:210571
Treatments0 drug(s)
Symptoms on record15 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO