Eales disease

ICD-10: H35.0MeSH: C538011ORPHA: 40923

Overview

Eales disease (ED) is an idiopathic, inflammatory retinal venous occlusive disease characterized by 3 stages: vasculitis, occlusion and retinal neovascularization, leading to recurrent vitreous hemorrhages and vision loss

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with Eales disease, sourced from HPO and Orphanet clinical annotations.

HeadacheVitreous hemorrhageRetinal vasculitisEpistaxisGlaucomaOptic disc pallorBlindnessAbnormality of the nervous systemConstipationSpastic paraparesisMultifocal cerebral white matter abnormalitiesReduced visual acuityTractional retinal detachmentRubeosis iridisCystoid macular edemaVitritisAnterior uveitisRhegmatogenous retinal detachmentRetinal thinning on OCTVitreous hazePeripheral retinal neovascularizationInternuclear ophthalmoplegiaPhotopsiaMacular edemaVitreous floatersIschemic strokeMyelopathyTransient ischemic attackPreretinal hemorrhageEpiretinal membrane

Classification & Codes

ICD-10 Code

H35.0

MeSH Code

C538011

Orphanet Code

ORPHA:40923
Eales disease
ICD-10H35.0
MeSHC538011
OrphanetORPHA:40923
Treatments0 drug(s)
Symptoms on record30 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO
Eales disease | OrphanDrug