Ebstein anomaly

MeSH: D004437ORPHA: 1880

Overview

tricuspid valve disease that is a congenital heart defect in which the septal leaflet of the tricuspid valve is displaced towards the apex of the right ventricle of the heart

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with Ebstein anomaly, sourced from HPO and Orphanet clinical annotations.

Premature birthAtrial septal defectRespiratory insufficiencyEbstein anomaly of the tricuspid valveImperforate tricuspid valveFatigueAbnormal cardiovascular system morphologyCyanosisPatent ductus arteriosusAbnormal cardiac septum morphologyPalpitationsAtrial fibrillationTricuspid regurgitationArrhythmiaComplete right bundle branch blockHolosystolic murmurChest painCongestive heart failureSudden cardiac deathDyspneaCerebral ischemiaAbnormal endocardium morphologyArterial thrombosisPedal edemaHypoxemiaStrokeMyocardial infarction

Classification & Codes

MeSH Code

D004437

Orphanet Code

ORPHA:1880
Ebstein anomaly
MeSHD004437
OrphanetORPHA:1880
Treatments0 drug(s)
Symptoms on record27 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO