Ehlers-Danlos syndrome, cardiac valvular type

MeSH: C536200ORPHA: 230851

Available Treatments (0)

No treatments linked yet

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Clinical Presentation

Signs and symptoms associated with Ehlers-Danlos syndrome, cardiac valvular type, sourced from HPO and Orphanet clinical annotations.

Hyperextensible skinJoint hypermobilityMitral regurgitationAbnormal heart valve morphologyInguinal herniaStrabismusPtosisMyopiaDental crowdingPectus excavatumThin skinBruising susceptibilitySoft, doughy skinPoor wound healingAtrophic scarsJoint dislocationAortic regurgitationPes planusHallux valgusAortic root aneurysmGenu recurvatumGenu valgumTricuspid regurgitationAbsent phalangeal creaseHypermobility of distal interphalangeal jointsLong fingersHigh palateBulbous noseThick eyebrowSeizureGlobal developmental delayDisproportionate tall statureAtrial septal defectMitral valve prolapseLeft ventricular hypertrophyCalcaneovalgus deformitySandal gapDyspneaModerate intellectual disabilityKyphoscoliosisThoracolumbar scoliosisShort staturePulmonic regurgitationFatigueSevere conductive hearing impairmentRecurrent shoulder dislocationTendon thickeningTendon ruptureMyopic astigmatism

Classification & Codes

MeSH Code

C536200

Orphanet Code

ORPHA:230851
Ehlers-Danlos syndrome, cardiac valvular type
MeSHC536200
OrphanetORPHA:230851
Treatments0 drug(s)
Symptoms on record49 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO