Ehlers-Danlos syndrome, musculocontractural type

MeSH: C000600608ORPHA: 2953

Available Treatments (0)

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Clinical Presentation

Signs and symptoms associated with Ehlers-Danlos syndrome, musculocontractural type, sourced from HPO and Orphanet clinical annotations.

CryptorchidismNarrow mouthHigh palateThin upper lip vermilionLarge fontanellesHypertelorismLong philtrumMacrotiaProtruding earDownslanted palpebral fissuresBlue scleraeAbnormal sternum morphologyHyperextensible skinBruising susceptibilityAtrophic scarsSlender fingerMuscle weaknessDisproportionate tall statureAbnormal bleedingSubcutaneous hemorrhageDelayed gross motor developmentScoliosisGeneralized joint hypermobilityArthrogryposis multiplex congenitaShort noseDecreased muscle massAbnormality of the cervical spineProminent nasolabial foldDecreased palmar creasesDysesthesiaRecurrent joint dislocationMicroretrognathiaAstigmatismStrabismusRetinal detachmentMyopiaTapered fingerRecurrent skin infectionsRedundant skinConstipationKyphoscoliosisCervical kyphosisMyopathyOcular hypertensionThoracic lordosisFunctional abnormality of the bladderHydronephrosisCleft palateHearing impairmentGlaucomaNephrolithiasisCraniosynostosisAbnormal heart morphologyAbnormal heart valve morphologyPneumothoraxVentriculomegalyAtlantoaxial dislocationAbnormal mesentery morphologyCleft lipInguinal herniaHorseshoe kidneyMalrotation of small bowelPosteriorly rotated earsAbnormal pinna morphology

Classification & Codes

MeSH Code

C000600608

Orphanet Code

ORPHA:2953
Ehlers-Danlos syndrome, musculocontractural type
MeSHC000600608
OrphanetORPHA:2953
Treatments0 drug(s)
Symptoms on record64 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO