Eisenmenger's syndrome
ICD-10: Q21.8ORPHA: 97214
Overview
fetal heart defect
Available Treatments (0)
No treatments linked yet
Clinical trials or compassionate use may be available — consult a specialist.
Clinical Presentation
Signs and symptoms associated with Eisenmenger's syndrome, sourced from HPO and Orphanet clinical annotations.
Abnormal heart morphologyPulmonary arterial hypertensionExercise intoleranceMuscle weaknessPalpitationsExertional dyspneaSupraventricular tachycardiaAtrial fibrillationSupraventricular arrhythmiaIncreased pulmonary vascular resistanceFatigueHypoxemiaHeart murmurCyanosisClubbingLethargyAbnormality of the liverAscitesHoarse voiceVentricular septal defectAtrial septal defectPatent ductus arteriosusAngina pectorisRight-to-left shuntRight ventricular failureIron deficiency anemiaRespiratory distressHemoptysisHepatomegalyAbdominal distentionVentricular tachycardiaHypochromic microcytic anemiaTricuspid regurgitationAtrioventricular canal defectPedal edemaElevated circulating C-reactive protein concentrationAortopulmonary windowComplete right bundle branch blockLeft-to-right shuntPeripheral edemaElevated jugular venous pressureHepatojugular refluxAbnormal circulating B-type natriuretic peptide concentrationChest painRenal insufficiencySyncopeStrokeTetralogy of FallotAbnormal bleedingHyperuricemiaVertigoVentricular arrhythmiaIncreased mean corpuscular volumeBacterial endocarditisGeneralized edemaBrain abscessWheezingHypercoagulability
Classification & Codes
ICD-10 Code
Q21.8Orphanet Code
ORPHA:97214Eisenmenger's syndrome
| ICD-10 | Q21.8 |
| Orphanet | ORPHA:97214 |
| Treatments | 0 drug(s) |
| Symptoms on record | 58 signs |
| Status | published |
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO