epidermolysis bullosa simplex with anodontia/hypodontia

ORPHA: 2325

Overview

human disease

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with epidermolysis bullosa simplex with anodontia/hypodontia, sourced from HPO and Orphanet clinical annotations.

Abnormality of the faceMandibular prognathiaShort philtrumHearing impairmentMyopiaAbnormal dental enamel morphologyDelayed eruption of teethEctopia lentisAbnormal fingernail morphologyAlopeciaHypoplastic toenailsAnemiaSparse scalp hairFatigable weaknessAbnormal blistering of the skinTooth agenesisCognitive impairmentToenail dysplasiaFingernail dysplasia

Classification & Codes

Orphanet Code

ORPHA:2325
epidermolysis bullosa simplex with anodontia/hypodontia
OrphanetORPHA:2325
Treatments0 drug(s)
Symptoms on record19 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO