erythrokeratodermia variabilis

MeSH: D056266ORPHA: 317

Overview

human disease

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with erythrokeratodermia variabilis, sourced from HPO and Orphanet clinical annotations.

MicrocephalyHyperkeratosisSkin rashCutaneous photosensitivityHypermelanotic maculeWeight lossShort statureAbnormal blistering of the skinErythemaMaculeGlaucomaCataractDiabetes mellitusDry skinAbnormal hair morphologyAlopeciaPatchy palmoplantar hyperkeratosisIrregular hyperpigmentationAbnormal testis morphologyHearing impairmentProtruding earBrachydactylyTapered fingerIntellectual disabilityAbnormal nail morphologyGeneralized hirsutismCorneal opacityNeoplasm of the skinAbnormal cardiovascular system morphology

Classification & Codes

MeSH Code

D056266

Orphanet Code

ORPHA:317
erythrokeratodermia variabilis
MeSHD056266
OrphanetORPHA:317
Treatments0 drug(s)
Symptoms on record29 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO