familial adenomatous polyposis due to 5q22.2 microdeletion

ORPHA: 261584

Overview

human disease

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with familial adenomatous polyposis due to 5q22.2 microdeletion, sourced from HPO and Orphanet clinical annotations.

Adenomatous colonic polyposisNarrow mouthThick upper lip vermilionHigh palateLong faceMandibular prognathiaHypertelorismLong philtrumHigh foreheadBroad nasal tipDownslanted palpebral fissuresMild intellectual disabilityIron deficiency anemiaEarly baldingIntestinal bleedingRelative macrocephalyDuodenal polyposisCongenital hypertrophy of retinal pigment epitheliumDyslexiaAbnormality of canineEpidermoid cystMicrognathiaShort neckSingle transverse palmar creasePosterior polar cataractGeneralized hypotoniaSpastic gaitLow posterior hairlineColon cancerAirway obstructionOptic disc hypoplasiaGastrointestinal desmoid tumorAbnormality of the kidneyHepatoblastomaOsteoma

Classification & Codes

Orphanet Code

ORPHA:261584
familial adenomatous polyposis due to 5q22.2 microdeletion
OrphanetORPHA:261584
Treatments0 drug(s)
Symptoms on record35 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO