familial erythrocytosis 1

ORPHA: 90042

Overview

Human disease

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with familial erythrocytosis 1, sourced from HPO and Orphanet clinical annotations.

EpistaxisPruritusAbnormal bleedingPolycythemiaThromboembolismAbdominal painDyspneaHeadacheVertigoArthralgiaExertional dyspneaVenous thrombosisAbnormal hemoglobinFatigueCough

Classification & Codes

Orphanet Code

ORPHA:90042
familial erythrocytosis 1
OrphanetORPHA:90042
Treatments0 drug(s)
Symptoms on record15 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO
familial erythrocytosis 1 | OrphanDrug