familial idiopathic dilatation of the right atrium

ORPHA: 1677

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with familial idiopathic dilatation of the right atrium, sourced from HPO and Orphanet clinical annotations.

Atrial septal dilatationRight atrial enlargementSyncopeCardiomegalyRight ventricular hypertrophyAtrioventricular blockPalpitationsDyspneaAtrial fibrillationComplete heart block with narrow QRS complexesTricuspid regurgitationAbnormal vena cava morphologyAbnormality of the hepatic vasculatureArrhythmiaReduced left ventricular ejection fractionAbnormal cardiac ventricular functionMidsystolic murmurHolosystolic murmurSeizurePleural effusionHepatomegalyParoxysmal atrial fibrillationPeripheral edemaAbnormal jugular vein morphology

Classification & Codes

Orphanet Code

ORPHA:1677
familial idiopathic dilatation of the right atrium
OrphanetORPHA:1677
Treatments0 drug(s)
Symptoms on record24 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO