familial isolated dilated cardiomyopathy

ORPHA: 154

Overview

Familial isolated dilated cardiomyopathy is a rare, genetically heterogeneous cardiac disease characterized by dilatation leading to systolic and diastolic dysfunction of the left and/or right ventricles, causing heart failure or arrhythmia

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with familial isolated dilated cardiomyopathy, sourced from HPO and Orphanet clinical annotations.

Dilated cardiomyopathyLeft ventricular systolic dysfunctionEdemaCongestive heart failureExertional dyspneaArrhythmiaFatigueOrthopneaSensorineural hearing impairmentThromboembolic strokeMyopathyEMG abnormalityLipoatrophy

Classification & Codes

Orphanet Code

ORPHA:154
familial isolated dilated cardiomyopathy
OrphanetORPHA:154
Treatments0 drug(s)
Symptoms on record13 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO
familial isolated dilated cardiomyopathy | OrphanDrug