familial partial lipodystrophy type 6

ORPHA: 435660

Overview

familial partial lipodystrophy characterized by autosomal recessive inheritance that has material basis in mutation in the LIPE gene on chromosome 19q13

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with familial partial lipodystrophy type 6, sourced from HPO and Orphanet clinical annotations.

Increased adipose tissue around the neckInsulin resistanceLoss of subcutaneous adipose tissue in limbsLipodystrophyPolycystic ovariesInsulin-resistant diabetes mellitusOligomenorrheaAcanthosis nigricansHepatic steatosisHypertriglyceridemiaHepatomegalyElevated circulating creatine kinase concentrationDecreased serum leptinSkeletal muscle hypertrophyIncreased intraabdominal fatLoss of gluteal subcutaneous adipose tissueAbnormal labia majora morphologyDecreased adiponectin levelProximal lower limb muscle weaknessProximal upper limb muscle weakness

Classification & Codes

Orphanet Code

ORPHA:435660
familial partial lipodystrophy type 6
OrphanetORPHA:435660
Treatments0 drug(s)
Symptoms on record20 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO