familial visceral amyloidosis

ICD-10: E85.0MeSH: C538249ORPHA: 85450

Overview

type of amyloidosis that mostly affects the kidney

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with familial visceral amyloidosis, sourced from HPO and Orphanet clinical annotations.

ProteinuriaNephropathyRenal interstitial amyloid depositsRenal insufficiencyHypertensionTubulointerstitial nephritisElevated circulating creatinine concentrationAbnormality of the gastrointestinal tractDecreased glomerular filtration rateAbnormal urinary electrolyte concentrationNocturiaRenal tubular atrophyNephrotic syndromePetechiaePurpuraDecreased liver functionHepatosplenomegalyCongestive heart failureWeight lossAnemiaVomitingDiarrheaNauseaGastroesophageal refluxAbdominal painGastrointestinal hemorrhageHepatomegalyLymphadenopathyAbnormal lymph node morphologyMyopathyDecreased HDL cholesterol concentrationElevated erythrocyte sedimentation rateIntestinal obstructionTubulointerstitial fibrosisPeripheral neuropathyIntestinal perforationDecreased circulating apolipoprotein A-I concentrationDyspepsiaAbnormal testis morphologyHypogonadismOligozoospermiaMale infertilityPrimary testicular failure

Classification & Codes

ICD-10 Code

E85.0

MeSH Code

C538249

Orphanet Code

ORPHA:85450
familial visceral amyloidosis
ICD-10E85.0
MeSHC538249
OrphanetORPHA:85450
Treatments0 drug(s)
Symptoms on record43 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO
familial visceral amyloidosis | OrphanDrug