febrile infection-related epilepsy syndrome

ICD-10: G40.5ORPHA: 163703

Contents

1. Overview
2. Available Treatments
3. Clinical Presentation
4. Classification & Codes

Overview

an explosive-onset, potentially fatal acute epileptic encephalopathy that develops in previously healthy children and adolescents following the onset of a non-specific febrile illness

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with febrile infection-related epilepsy syndrome, sourced from HPO and Orphanet clinical annotations.

SinusitisAtypical behaviorLethargySudden deathFeverHeadacheEEG abnormalityDevelopmental regressionAutoimmunityMyalgiaFocal-onset seizureCough

Classification & Codes

ICD-10 Code

G40.5

Orphanet Code

ORPHA:163703

febrile infection-related epilepsy syndrome

ICD-10	`G40.5`
Orphanet	`ORPHA:163703`
Treatments	0 drug(s)
Symptoms on record	12 signs
Status	published

Factual Authority

Last Updated3/20/2026

Clinical DataHPO · Orphanet

Drug DataFDA · EMA · CDSCO