FGFR2-related bent bone dysplasia

ORPHA: 313855

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with FGFR2-related bent bone dysplasia, sourced from HPO and Orphanet clinical annotations.

Gingival overgrowthHypertelorismMicrognathiaAbnormality of the outer earLow-set earsMegalocorneaNatal toothShort claviclesOsteopeniaHirsutismBrachydactylyBell-shaped thoraxExtramedullary hematopoiesisHypoplastic ischiaCoronal craniosynostosisOverfolding of the superior helicesDecreased calvarial ossificationEarly-onset non-progressive night blindnessClitoral hypertrophySteep acetabular roofMetopic depressionMidface retrusionIncomplete ossification of pubisAbnormal periosteum morphologyHepatosplenomegalyAbnormality of the lower limbBowing of the legs

Classification & Codes

Orphanet Code

ORPHA:313855
FGFR2-related bent bone dysplasia
OrphanetORPHA:313855
Treatments0 drug(s)
Symptoms on record27 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO