fibronectin glomerulopathy

MeSH: C536826ORPHA: 840901 Treatment Available

Overview

Fibronectin glomerulopathy is a hereditary kidney disease characterized by proteinuria, type IV renal tubular acidosis, microscopic hematuria and hypertension that may lead to end-stage renal failure in the second to sixth decade of life

Available Treatments (1)

DrugFormStatusCountriesLead Time
Tacrolimus
Capsule, Tablet, IV solutionFDA Approved57d

Clinical Presentation

Signs and symptoms associated with fibronectin glomerulopathy, sourced from HPO and Orphanet clinical annotations.

Renal insufficiencyProteinuriaNephrotic syndromeHypertensionCerebral hemorrhageAbnormal glomerular mesangium morphologyMicroscopic hematuriaHypoalbuminemiaPedal edemaGlomerulopathy

Classification & Codes

MeSH Code

C536826

Orphanet Code

ORPHA:84090
fibronectin glomerulopathy
MeSHC536826
OrphanetORPHA:84090
Treatments1 drug(s)
Symptoms on record10 signs
Statuspublished

Treatment Summary

Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO