Frontorhiny

ORPHA: 391474

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with Frontorhiny, sourced from HPO and Orphanet clinical annotations.

Cleft palateEpicanthusHypertelorismHypoplasia of the maxillaWidow's peakPosteriorly rotated earsPreauricular skin tagStrabismusPtosisCataractMicrophthalmiaIris colobomaBrachydactylyEncephaloceleScoliosisHypoplastic frontal sinusesLumbar hyperlordosisMidline nasal grooveCranium bifidum occultumPericallosal lipomaAplasia/Hypoplasia of the corpus callosumCongenital conductive hearing impairmentBifid tongueBasal encephaloceleDermoid cystFinger clinodactylyCamptodactyly of fingerDiabetes insipidusHypopituitarism

Classification & Codes

Orphanet Code

ORPHA:391474
Frontorhiny
OrphanetORPHA:391474
Treatments0 drug(s)
Symptoms on record29 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO